An unusual Cause of upper airway obstruction in newborn: Congenital nasal pyriform aperture stenosis


An unusual Cause of upper airway obstruction in newborn: Congenital nasal pyriform aperture stenosis


Omar Iziki*, Sami Rouadi, Redallah larbi Abada, Mohamed Roubal, Mohamed Mahtar

Department of Otorhinolaryngology, Head and Neck Surgery, King Hassan II University and Ibn Rochd Hospital, Morocco


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Congenital nasal pyriform aperture stenosis (CNAPS) is a rare cause of pediatric nasal airway obstruction that clinically mimics choanal atresia in a neonate. CNPAS is suspected clinically and confirmed with CT scanning. Early diagnosis and management is essential for this potentially life-threatening condition. Because of the association this anomaly has with other midline defects, such as holoprosencephaly, it is important to recognize it and pursue a thorough workup. Patients can be managed conservatively or surgically. Surgical treatment is usually reserved for those patients that fail conservative treatment. We present a case of CNPAS, to highlight the importance of recognizing the classic signs of CNPAS on cross-sectional imaging to prevent fatal outcome.


Keywords: Nasal obstruction, pyriform aperture stenosis, congenital, megaincisor.

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How to cite this article:

Omar Iziki, Sami Rouadi, Redallah larbi Abada, Mohamed Roubal, Mohamed Mahtar.An unusual Cause of upper airway obstruction in newborn: Congenital nasal pyriform aperture stenosis. International Journal of Case Reports, 2019 4: 77. DOI: 10.28933/ijcr-2019-02-2205 (This article has been withdrawn from International Journal of Case Reports. Please do not use it for any purpose)


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